Document Type : Case Report

Authors

1 Associated Professor of Clinical Cardiac Electrophysiology, Shiraz University of medical science, Non-communicable disease research center, Shiraz, Iran

2 Department of Cardiology, Shiraz University of Medical Sciences, Shiraz, Iran

3 Professor of Clinical Cardiac Electrophysiology, Rajaie Cardiovascular, Medical and Research Center, Tehran, Iran

4 Department of Cardiology Medicine, Shiraz University of Medical Sciences, Shiraz, Iran

5 Department of Cardiology Medicine, Shiraz University of Medical Science, Shiraz, Iran

6 Faculty of Medicine, Shiraz University of Medical Sciences, Shiraz, Iran

7 Assistant Professor of Cardiology, Department of Cardiology Medicine, Shiraz University of medical science, Shiraz, Iran

10.48305/arya.2023.11842.0

Abstract

Electrical storm can be caused by structural heart disease and/or functional electrical abnormalities. We report a young boy without cardiac risk factors, having positive family history of sudden cardiac death who presented with electrical storm. Stepwise diagnostic approach was not fruitful to determine previously known causes as the origin of the electrical storm. A new genotype related to the current electrical storm has been found, and intracardiac pacing ceased it.

Keywords