Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report

Di Liberto, Ilenia; Pilato, Gerlando; Caramanno, Giuseppe

doi:10.48305/arya.2022.11722.2343

Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report

Document Type : Case Report

Authors

Ilenia Di Liberto

Gerlando Pilato

Giuseppe Caramanno

Department of Interventional Cardiology, San Giovanni Di Dio Hospital, Agrigento, Italy

https://doi.org/10.48305/arya.2022.11722.2343

Abstract

Background: Ehlers-Danlos syndrome (EDS) is a hereditary collagen vascular disorder characterized by joint hypermobility, skin hyperextensibility, and tissue fragility. Vascular EDS (vEDS) is a subtype of EDS which is characterized by vascular fragility.
Case presentation: This is a case report of a young man with vEDS hospitalized for myocardial infarction. He was presented with a coronary dissection and developed aortic dissection, coronary rupture, and cardiac tamponade until death.
Conclusion: This case report highlights how patients with vEDS and acute coronary syndrome show a higher risk of vascular complications compared with other patients, and their admission to the institution with a cardiac surgery room could be helpful and safe for better management of the complications. Non-invasive methods could be useful to exclude other vascular diseases, before the emergency coronary intervention.

Highlights

The PubMed Links for Di Liberto Ilenia

PubMed

Keywords

Vascular Ehlers-Danlos syndrome

Acute coronary syndrome

Coronary dissection

Aortic dissection

Coronary rupture

Cardiac tamponade

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