ARYA Atherosclerosis Journal

Report of persistent left superior vena cava associated with Ebstein’s anomaly of tricuspid valve

Document Type : Case Report

Authors

Zahra Khajali 1
Maryam Aliramezany 2

1 Professor, Adult Congenital Heart Diseases, Rajaie Cardiovascular, Medical, and Research Center, Iran University of Medical Sciences, Tehran, Iran

2 Assistant Professor, Adult Congenital Heart Diseases, Cardiovascular Research Center, Institute of Basic and Clinical Physiology Sciences, Kerman University of Medical Sciences, Kerman, Iran

https://doi.org/10.22122/arya.v17i0.2287
Abstract
BACKGROUND: Ebstein’s anomaly is one of the challenging congenital heart diseases (CHDs) that is presented with different anatomical and clinical symptoms. For this reason, patients with this complication require exact diagnostic methods and appropriate treatment approaches. In addition, multiple cardiac defects accompany this anomaly.CASE REPORT: In this study, we describe a rare associated defect in an adult patient with Ebstein’s anomaly and proper surgical methods performed for her.CONCLUSION: The most important issue in adult patients with Ebstein’s anomaly is to pay close attention to the presence of associated anomalies, in which careful examination and use of para-clinical methods is very helpful. Furthermore, accurate diagnosis of the associated defects determines the treatment and surgery of patients.

Keywords

Ebstein Anomaly
Heart Defects
Congenital
Left Superior Vena Cava
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ARYA Atherosclerosis Journal
Volume 17, Issue 1
January and February 2021
Pages 1-4

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