ARYA Atherosclerosis Journal

Isolated double-orifice mitral valve in a young girl

Document Type : Case Report

Authors

Niloufar Samiei 1
Hooman Dehghan 2
Maryam Pourmojib 3
Ahmad Mohebbi 4
Saeid Hosseini 4
Yousef Rezaei 3

1 Associate Professor, Heart Valve Disease Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran

2 Cardiologist, Heart Valve Disease Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran

3 Heart Valve Disease Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran

4 Professor, Heart Valve Disease Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran

Abstract
BACKGROUND: Double-orifice mitral valve (DOMV) is an extremely rare cardiac malformation. It has been found to be accompanied by congenital anomalies (CAs), however, it can be detected as an isolated anomaly. The clinical findings of a DOMV are variable and depend predominantly on the associated cardiac abnormalities, particularly atrioventricular septal defects or mitral valve (MV) regurgitation and/or stenosis. CASE REPORT: In this regard, we describe an isolated DOMV in an 18-year-old young girl who complained of a short-term nonspecific chest pain. She underwent transthoracic and transesophageal echocardiographic examinations. The examinations revealed a DOMV without any valvular or structural malformations. Other examinations were unremarkable. The patient did need neither medical nor surgical interventions. CONCLUSION: The isolated cases of DOMV do not need therapy and might be only followed up using echocardiographic examinations. However, a careful echocardiographic examination for detection of concomitant structural malformations would be of great importance in the management of such cases. 

Keywords

Double Orifice Mitral Valve
Mitral Valve Disease
Congenital Heart DiseaseEchocardiography, Heart Valve Disease
Mitral Valve
Congenital Heart Defects
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ARYA Atherosclerosis Journal
Volume 13, Issue 6 - Serial Number 6
November and December 2017
Pages 295-298

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